EA/TEF Quiz / EUPSA Quizzes / By EUPSA Welcome to your Esophageal Atresia / Tracheo-esophageal Fistula Operative management of a newborn with Type C Esophageal Atresia / Tracheoesophageal Fistula should occur: Immediately after Birth Within 24 hours Within 72 hours In the NICU None of the above None The most common form of esophageal atresia (EA) is: H- or N-type fistula Pure tracheoesophageal fistula TEF (no atresia) EA with distal TEF EA with proximal TEF EA with proximal and distal TEF None What is the most typical presentation of a newborn with Esophageal Atresia with a Tracheoesophageal Fistula? A baby who… is drooling and has abnormal respiratory sounds at one hour old. was large for gestational age, has crepitus at his collar bone, and is not moving his right arm. has a temperature of 100.9 and high heart and respiratory rates. was born at 34 weeks gestation and has low blood sugar. who has a cyanotic heart disease at birth. None Spontaneous intrauterine fetal demise occurs in how many % of cases with esophageal atresia/ tracheoesophaeal fistula (EA/TEF)? 30% 20% 10% 5% less than 3% None Most infants with EA will have at least one other associated anomaly, which is the most common one Cardiac Renal Limb Anorectal Vertebral None Which statement on prenatal diagnosis in EA/TEF is true? 50% in patients with EA/TEF 10% in patients with isolated EA 90% in patients with isolated EA Indicative of EA is include polyhydramnios, a small or absent stomach bubble, and a dilated upper esophageal pouch (“pouch sign”). The sensitivity and specificity of prenatal diagnosis are not significantly improved with MRI over ultrasound. None How is long gap atresia defined and what is its impact on management? There is no general accepted definition 3cm in a newborn 3 vertebral bodies in the newborn 2-5 vertebral bodies in the newborn All cases without tracheoesophageal fistula None How do outcomes of thoracoscopic versus standard thoracotomy approaches compare for EA/TEF repair? Less anastomotic stenosis following thoracoscopic repair Less anastomotic leakage following thoracoscopic repair Less long-term respiratory morbidity following thoracoscopic repair no differences in outcomes including anastomotic leak rate, esophageal stricture rate, pulmonary complications Open repair has lower mortality None What are surgical options for long gap EA if primary esophagoesophagostomy is not possible? placement of a gastrostomy tube followed by delayed primary repair esophageal lengthening with circular or spiral myotomy Kimura extrathoracic lengthening procedure Foker staged suture-traction All of the above None What postoperative complications are most common following EA/TEF repair? recurrent fistula anastomotic leak anastomotic stricture vocal cord paralysis chylothorax None Time's up
